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Superstiti di Malattie Congenite del Cuore Cianotico: Una Revisione.

Egidy Assenza G, O'Leary E, Brida M, Kwon M, Landzberg MJ

JAMA·1 giugno 2026·DOI ↗

IMPORTANCE: Cyanotic congenital heart diseases, which occur in approximately 0.2% of live births in the United States, have high mortality rates if untreated, but survival to adulthood is common with current surgical interventions. OBSERVATIONS: Approximately 80% of all cyanotic congenital heart diseases are caused by tetralogy of Fallot (TOF), D-loop transposition of the great arteries (TGA), and congenital heart disease with single-ventricle circulation. Survivors of cyanotic congenital heart diseases benefit from multidisciplinary care including pediatric and adult cardiologists, congenital cardiac surgeons, and electrophysiologists. Ninety percent of patients with TOF survive more than

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