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Case Report

Dysplasia fibrosa nella craniosinostosi.

Middleton L, Shanmuganathan P, Anderson P

The Journal of craniofacial surgery·1 maggio 2026·DOI ↗

PURPOSE: This case series presents 2 pediatric patients diagnosed with craniosynostosis who subsequently developed fibrous dysplasia. The aim is to describe their clinical presentation, management, and outcomes. METHODS: A retrospective chart review was conducted at Cleft and Craniofacial SA, Women's and Children's Hospital, Adelaide, South Australia. Medical histories, examinations, imaging, and longitudinal follow-up data were analyzed. RESULTS: Two patients with craniosynostosis with fibrous dysplasia were identified. Firstly, a 13-year-old male with sagittal synostosis, underwent cranial vault remodeling at 7 months of age. The second patient, a 16-year-old female with metopic synostos

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